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Title | 低ホスファターゼ症(HPP)の医学的リソース |
Description | HPPは、生命を脅かす全身性の遺伝性代謝性疾患です1,8 低ホスファターゼ症(HPP)は、骨、全身、生命に影響を及ぼします。最新の臨床的洞察、症状、診断、 |
Keywords | HPP,低ホスファターゼ症,希少骨疾患,症状,診断, 治療 |
WebSite | hppsource.jp |
Host IP | 52.85.47.114 |
Location | United States |
Site | Rank |
US$600,443
Last updated: 2022-10-07 01:05:16
hppsource.jp has Semrush global rank of 17,627,502. hppsource.jp has an estimated worth of US$ 600,443, based on its estimated Ads revenue. hppsource.jp receives approximately 69,282 unique visitors each day. Its web server is located in United States, with IP address 52.85.47.114. According to SiteAdvisor, hppsource.jp is safe to visit. |
Purchase/Sale Value | US$600,443 |
Daily Ads Revenue | US$555 |
Monthly Ads Revenue | US$16,628 |
Yearly Ads Revenue | US$199,532 |
Daily Unique Visitors | 4,619 |
Note: All traffic and earnings values are estimates. |
Host | Type | TTL | Data |
hppsource.jp. | A | 60 | IP: 52.85.47.114 |
hppsource.jp. | A | 60 | IP: 52.85.47.73 |
hppsource.jp. | A | 60 | IP: 52.85.47.15 |
hppsource.jp. | A | 60 | IP: 52.85.47.65 |
hppsource.jp. | NS | 21600 | NS Record: ns-1021.awsdns-63.net. |
hppsource.jp. | NS | 21600 | NS Record: ns-1183.awsdns-19.org. |
hppsource.jp. | NS | 21600 | NS Record: ns-1554.awsdns-02.co.uk. |
hppsource.jp. | NS | 21600 | NS Record: ns-413.awsdns-51.com. |
hppsource.jp. | TXT | 300 | TXT Record: google-site-verification=uP6SM79wevPwFoUqZGmzpN3EPiyqQhcK53OU7JAlluY |
hppsource.jp. | TXT | 300 | TXT Record: pardot950442=6589c62235a54a64b89205ebbb89ba61f7224b05f3eaababbb501199c0f4d20c |
患者さんとそのご家族の方向けサイトはこちら Ruins Bodies, Bones, And Lives. --> HPP HPPの影響 疾患のメカニズム 年齢を問わず発症する症状 全身性の症状 骨格系 呼吸器系 神経系 腎臓 筋肉/関節 HPPの診断 診断 年齢別基準値に注意したALP 正確な診断の重要性 よくある見過ごし 治療 治療 外科治療 リソース 臨床ビデオ 患者さん/ご家族の方向け資料 HPPは、生命を脅かす全身性の遺伝性代謝性疾患です 1,8 HPPは、あらゆる年齢の患者さんにおいて、重篤で生命にかかわる症状を伴います 1 「HPPの影響」について詳しくはこちら HPPは骨・全身に影響を及ぼします 1,7 PPiとPLPの蓄積は、衰弱性または生命を脅かす骨格系や全身性の症状の発症の原因となります 1,4,16-19 HPPに伴う骨格系障害およびその他の 全身性の症状について詳しくはこちら HPPの早期かつ正確な診断 早期かつ正確にHPPを診断することは、症状の発症と、若年死を防ぐ上で極めて重要です 11-13 HPPの診断について詳しくはこちら 本ウェブサイトに掲載した情報は教育のみを目的としており、専門家による医学的判断の代わりに用いることはできません References: 1. Rockman-Greenberg C. Hypophosphatasia. Pediatr Endocrinol Rev. 2013;10(suppl 2):380-388. 2. Baumgartner-Sigl S, Haberlandt E, Mumm S, et al. Pyridoxine-responsive seizures as the first symptom of infantile hypophosphatasia caused by two novel missense mutations (c.677T>C, p.M226T; c.1112C>T, p.T371I) of the tissue-nonspecific alkaline phosphatase gene. Bone . 2007;40(6):1655-1661. 3. Eade AWT, Swannell AJ, Williamson N. |
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